Key words:. Dorantes-Mesa S. Hereditary spherocytosis. An Esp Pediatr.

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Key words:. Dorantes-Mesa S. Hereditary spherocytosis. An Esp Pediatr. Congenital spherocytosis is often not hereditary. Clin Pediatr Phila. Natural history of hereditary spherocytosis during the first year of life. Christensen RD, Henry E. Hereditary spherocytosis in neonates with hyperbilirubinemia. Hereditary spherocytosis, elliptocytosis, and other red cell membrane disorders. Blood Rev. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.

Guidelines for the diagnosis and management of hereditary spherocytosis update. Br J Haematol. Severin CM. Anatomy of the spleen. Disorders of the spleen: pathophysiology and management. New York, NY: Dekker; Red-cell surface alterations in reticuloendothelial immaturity of the neonate. N Engl J Med. Rev Chil Pediatr. Neonatal hemolytic jaundice: morphologic features of erythrocytes that will help you diagnose the underlying condition.

A simple method of screening newborn infants for hereditary spherocytosis. J Applied Hematol. Decision making at the bedside: diagnosis of hereditary spherocytosis in a transfused infant. Rubin LG, Schaffner W. Clinical practice. Care of the asplenic patient. Infection with unexpected micro-organisms in splenectomised patients. Frequency of very late fatal sepsis after splenectomy for hereditary spherocytosis: impact of insufficient antibody response to pneumococcal infection.

Ann Hematol. Full text How to cite this article. Key words: Hereditary spherocytosis, hemolytic anemia, severe hyperbilirubinemia in the newborn, splenectomy in infants.


2012, NĂºmero 4

Hereditary spherocytosis is clinically and genetically heterogeneous disorder and its clinical characteristics are spherocytosis, anaemia, jaundice and splenomegaly. The aetiology is associated to the genes encoding proteins involved in the interaction between the erythrocyte membrane and the lipid bilayer. Among kidney disease, isolated cases of nephrotic syndrome due to membranoproliferative glomerulonephritis and macroscopic haematuria with proteinuria due to IgA nephropathy were previously reported in patients with SPTB deficiency.. Seven patients from the same family with spherocytosis were evaluated to assess the kidney failure presented in all affected adult patients..


2017, Number 4

Aka: Hereditary Spherocytosis , Minkowski-Chauffard syndrome. These images are a random sampling from a Bing search on the term "Hereditary Spherocytosis. Search Bing for all related images. Started in , this collection now contains interlinked topic pages divided into a tree of 31 specialty books and chapters. Content is updated monthly with systematic literature reviews and conferences. Although access to this website is not restricted, the information found here is intended for use by medical providers.

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